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  • Retroperitoneal yolk sac tumour encroaching the liver and adrenal gland with tumour thrombus in cavo-atrial region and hepatic veins

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Case Reports: Unusual association of diseases/symptoms
Retroperitoneal yolk sac tumour encroaching the liver and adrenal gland with tumour thrombus in cavo-atrial region and hepatic veins
  1. Pujana Kanneganti1,
  2. Anju Verma1,
  3. Basant Kumar1 and
  4. Neha Nigam2
  1. 1Pediatric Surgery, Sanjay Gandhi Post Graduate Institute of Medical Sciences, Lucknow, UP, India
  2. 2Pathology, Sanjay Gandhi Post Graduate Institute of Medical Sciences, Lucknow, UP, India
  1. Correspondence to Dr Anju Verma; anju_v2006{at}rediffmail.com

Abstract

Paediatric germ cell tumours (GCT) are rare tumours and are unique because of varied clinical presentation and locations. Yolk sac tumour is the predominant malignant histology and a serum marker; alpha fetoprotein is used to see treatment response and recurrent disease. It is extremely rare to find a retroperitoneal GCT with tumour thrombus extending up to the cavo-atrial region with involvement of the hepatic veins. We report a case of retroperitoneal yolk sac tumour (RPYST) with extension to the liver and right adrenal gland along with tumour thrombus in the inferior vena cava and in the right and middle hepatic veins. The child was operated after satisfactory response to chemotherapy. Excision of the tumour along with the right adrenal gland and around 5 cm of retro-hepatic caval resection was done. Inferior vena cava resection was tolerated without reconstruction. Currently child is disease-free and symptom-free at 22 months of follow-up with normal serum marker.

  • Paediatric oncology
  • Paediatric Surgery

https://doi.org/10.1136/bcr-2023-255968

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    Footnotes

    • Contributors Material preparation and data collection were performed by PK and AV. The first draft of the manuscript was written by PK. AV and BK commented on and revised previous versions of the manuscript. NN was involved in all histopathological workup. All authors (PK, AV, BK and NN) read and approved the final manuscript. The following authors gave final approval of the manuscript: PK, AV, BK, NN.

    • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

    • Case reports provide a valuable learning resource for the scientific community and can indicate areas of interest for future research. They should not be used in isolation to guide treatment choices or public health policy.

    • Competing interests None declared.

    • Provenance and peer review Not commissioned; externally peer reviewed.