You are here

Article Text

Article menu
Download PDFPDF
Urology
Von Hippel-Lindau syndrome with bilateral renal and an interaortocaval mass
  1. Faisal Masood Pirzada1,
  2. Shritosh Kumar2,
  3. Keshav Agarwal3 and
  4. Brusabhanu Nayak1
  1. 1Urology, AIIMS New Delhi, New Delhi, Delhi, India
  2. 2AIIMS New Delhi, New Delhi, Delhi, India
  3. 3Urology, All India Institute of Medical Sciences New Delhi, Ghaziabad, Uttar Pradesh, India
  1. Correspondence to Dr Brusabhanu Nayak; brusabhanu@gmail.com

Abstract

Patients with bilateral renal masses and an interaortocaval mass (IACM) present a complex scenario where, in addition to renal masses, management of the IACM adds to challenges in an already challenging case. A young man in his 30s presented with left flank pain, associated with loss of appetite, headache and sweating. The evaluation revealed multiple renal masses in the right kidney, a large mass in the left kidney and an IACM. Staged surgery revealed bilateral renal masses to be clear cell renal cell carcinoma (RCC) and the IACM as paraganglioma (PG). In bilateral RCC, should there be a retroperitoneal mass, PG should be strongly considered and ruled out in addition to the evaluation of Von Hippel-Lindau syndrome.

  • Urological cancer
  • von Hippel-Lindau Disease

https://doi.org/10.1136/bcr-2024-263804

    Request Permissions

    If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.

    View Full Text

    Footnotes

    • Contributors Study design: FMP and BN. Data acquisition: SK and KA. Data analysis: FMP and BN. Drafting of the manuscript: PFM and BN. Critical revision of the manuscript: BN. Guarantor: BN.

    • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

    • Case reports provide a valuable learning resource for the scientific community and can indicate areas of interest for future research. They should not be used in isolation to guide treatment choices or public health policy.

    • Competing interests None declared.

    • Provenance and peer review Not commissioned; externally peer reviewed.